Alagille syndrome

Case contributed by Dr Jayanth Keshavamurthy

Presentation

6-year-old male with Alagille syndrome, branch pulmonary artery stenosis and a left pulmonary artery (LPA) stent.

Patient Data

Age: 6
Gender: Male
X-ray

Stable appearance of the median sternotomy wires with the most inferior wire fractured. Stable pulmonary artery vascular stent. 

No focal areas of consolidation or pleural effusions are identified.

The cardiac silhouette is not enlarged

Case Discussion

Surgery initially, there after multiple cardiac interventions for PA stenosis with stents.

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Case information

rID: 51270
Published: 8th Feb 2017
Last edited: 14th Aug 2019
Inclusion in quiz mode: Included

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